Intra-peritoneal leiomyoma of the round ligament in a patient with Mayer-Rokitansky-Küster-Hauser (MRKH) syndrome


Leiomyoma, Mayer-Rokitansky-Küster-Hauser, Middle East, round ligament

Published online: Feb 12 2017

G. Salem Wehbe1, R. Bitar2, T. Zreik2, M. Samaha2, C. Walter3, Z. Sleiman4

Lebanese university, Faculty of Medical Sciences
Lebanese American university school of medicine
Geneva university
Lebanese American university school of medicine, the European Academy for Gynecological Surgery


Background: The occurrence of an extra-uterine leiomyoma, arising from the intra-peritoneal portion of the round ligament in a lady with Müllerian agenesis diagnosed at the age of forty is extremely rare. We report a case of this rare combination in a Middle Eastern woman.

Case: A 40 years old lady, primarily amenorrheic, presented to our clinic for an infertility consultation. The work- up showed features suggestive of Mayer-Rokitansky-Küster-Hauser (MRKH) syndrome with a leiomyoma arising from the intra-peritoneal part of the round ligament.